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VWF

VWF,即血管性血友病因子,別名包括vWF。它是一種由第12號(hào)染色體的短臂所編碼的糖蛋白,主要在內(nèi)皮細(xì)胞合成,也由巨核細(xì)胞生成。VWF的作用機(jī)制包括與血小板膜GPⅠb-Ⅸ復(fù)合物及內(nèi)皮下膠原結(jié)合,介導(dǎo)血小板在血管損傷部位的黏附,同時(shí)與因子Ⅷ結(jié)合,作為載體具有穩(wěn)定因子Ⅷ的作用。VWF在止血過(guò)程中發(fā)揮關(guān)鍵作用,其缺乏或功能異常會(huì)導(dǎo)致血管性血友病(VWD),是一種常見(jiàn)的先天性出血性疾病。此外,VWF還在調(diào)節(jié)機(jī)體炎性過(guò)程中扮演重要角色,與一系列心血管疾病如動(dòng)脈粥樣硬化、急性冠狀動(dòng)脈綜合征、心房顫動(dòng)等均關(guān)系密切。

熱銷(xiāo)產(chǎn)品

VWF Antibody (CSB-PA292051)

驗(yàn)證數(shù)據(jù)

CSB-PA292051

The image on the left is immunohistochemistry of paraffin-embedded Human colon cancer tissue using CSB-PA292051(VWF Antibody) at dilution 1/50, on the right is treated with fusion protein. (Original magnification: ×200)

CSB-PA292051

The image on the left is immunohistochemistry of paraffin-embedded Human lung cancer tissue using CSB-PA292051(VWF Antibody) at dilution 1/50, on the right is treated with fusion protein. (Original magnification: ×200)

VWF Antibodies

VWF for Homo sapiens (Human)

VWF Proteins

VWF Proteins for Bos taurus (Bovine)

VWF Proteins for Rattus norvegicus (Rat)

VWF Proteins for Mus musculus (Mouse)

VWF Proteins for Canis familiaris (Dog) (Canis lupus familiaris)

VWF Proteins for Sus scrofa (Pig)

VWF ELISA Kit

VWF ELISA Kit for Canis lupus familiaris (Dog) (Canis familiaris)

VWF ELISA Kit for Homo sapiens (Human)

VWF ELISA Kit for Mus musculus (Mouse)

VWF ELISA Kit for Sus scrofa (Pig)

VWF ELISA Kit for Rattus norvegicus (Rat)