ABCD1
ABCD1是一種定位于過氧化物酶體膜上的ATP結合盒式轉運蛋白，具有特定的結構和功能。它利用ATP水解的能量，將超長鏈脂肪酸轉運至過氧化物酶體進行β-氧化，維持細胞內脂質平衡。ABCD1的結構特點包括兩個核苷酸結合結構域和兩個跨膜結構域，這些結構域在底物結合時發(fā)生構象變化，實現(xiàn)底物的轉運。然而，當ABCD1功能障礙時，會導致超長鏈脂肪酸在細胞質基質中異常積累，從而引發(fā)X-連鎖腎上腺腦白質營養(yǎng)不良等神經退行性疾病。
熱銷產品
Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1)-VLPs
CSB-MP001068HU
ABCD1 Antibodies
ABCD1 for Homo sapiens (Human)
| 產品貨號 | 產品名稱 | 種屬反應性 | 應用類型 |
|---|---|---|---|
| CSB-PA001068GA01HU | ABCD1 Antibody | Human,Mouse,Rat | ELISA,WB,IHC |
| CSB-PA214656 | ABCD1 Antibody | Human | ELISA,WB |
| CSB-PA008163 | ABCD1 Antibody | Human | WB, ELISA |
| CSB-PA001068LA01HU | ABCD1 Antibody | Human | ELISA, IHC |
ABCD1 Proteins
ABCD1 Proteins for Homo sapiens (Human)
| 產品貨號 | 產品名稱 | 來源 |
|---|---|---|
| CSB-YP001068HU1 CSB-EP001068HU1 CSB-BP001068HU1 CSB-MP001068HU1 CSB-EP001068HU1-B |
Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
| CSB-CF001068HU | Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1) (Active) | in vitro E.coli expression system |
| CSB-MP001068HU | Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1)-VLPs | Mammalian cell |
